Abstract：
As a subtype of neurofibromatosis, the plexiform neurofibroma is a benign, autosomally inherited disorder and predisposed to tumour formation. However, life-threatening haemorrhage into facial plexiform neurofibroma is extremely rare.
In the current study, we showed a facial plexiform neurofibroma case with massive haemorrhage in the cranio-maxillofacial region. An emergent selective angiography of the external carotid artery was performed to identify the offending artery, which was then selectively occluded by the combination of detachable coils and Onyx-34. Thus, the minimally invasive drainage surgery was successfully performed to evacuate the haematoma.
We believe the endovascular embolization achieved its purpose by providing an initial salvage strategy for stopping active haemorrhage in plexiform neurofibroma, allowing surgeons to perform open surgery with lower complications rate.
In the current study, we showed a facial plexiform neurofibroma case with massive haemorrhage in the cranio-maxillofacial region. An emergent selective angiography of the external carotid artery was performed to identify the offending artery, which was then selectively occluded by the combination of detachable coils and Onyx-34. Thus, the minimally invasive drainage surgery was successfully performed to evacuate the haematoma.
We believe the endovascular embolization achieved its purpose by providing an initial salvage strategy for stopping active haemorrhage in plexiform neurofibroma, allowing surgeons to perform open surgery with lower complications rate.
摘要：
作为神经纤维瘤病的一种亚型,丛状神经纤维瘤是良性的,常染色体遗传性疾病和易患肿瘤形成。然而,危及生命的面部丛状神经纤维瘤出血极为罕见。
在目前的研究中,我们显示了一个面部丛状神经纤维瘤病例，并在颅颌面部区域大出血。对颈外动脉进行了紧急选择性血管造影，以确定有问题的动脉，然后被可拆卸线圈和Onyx-34的组合选择性地遮挡。因此，成功进行了微创引流手术以清除血肿。
我们相信血管内栓塞通过提供阻止丛状神经纤维瘤活动性出血的初步抢救策略达到了目的。允许外科医生以更低的并发症率进行开放手术。
在目前的研究中,我们显示了一个面部丛状神经纤维瘤病例，并在颅颌面部区域大出血。对颈外动脉进行了紧急选择性血管造影，以确定有问题的动脉，然后被可拆卸线圈和Onyx-34的组合选择性地遮挡。因此，成功进行了微创引流手术以清除血肿。
我们相信血管内栓塞通过提供阻止丛状神经纤维瘤活动性出血的初步抢救策略达到了目的。允许外科医生以更低的并发症率进行开放手术。
