关键词: Pediatric Intestinal Pseudo-Obstruction antroduodenal manometry autoimmune GI dysmotility intestinal transplantation myopathy neuropathy

来  源:   DOI:10.3389/fped.2022.837462   PDF(Pubmed)

Abstract:
UNASSIGNED: Chronic intestinal pseudo-obstruction is a rare disorder and represents the most severe form of gastrointestinal dysmotility with significant morbidity and mortality. Emerging research shows considerable differences between the adult and pediatric population with intestinal pseudo-obstruction and the term Pediatric Intestinal Pseudo-Obstruction (PIPO) was recently proposed.
UNASSIGNED: The aim of this article is to provide pediatric gastroenterologists and pediatricians with an up to date review of the etiology and underlining pathophysiology, clinical features, diagnostic and management approaches currently available for PIPO and to discuss future perspectives for the diagnosis and management of this rare disease.
摘要:
未经证实:慢性肠道假性梗阻是一种罕见疾病,是最严重的胃肠道动力障碍,具有显著的发病率和死亡率。新兴研究表明,患有肠道假性梗阻的成人和儿童人群之间存在相当大的差异,最近提出了术语小儿肠道假性梗阻(PIPO)。
UNASSIGNED:本文的目的是为儿科胃肠病学家和儿科医生提供病因和病理生理学的最新综述,临床特征,PIPO目前可用的诊断和管理方法,并讨论这种罕见疾病的诊断和管理的未来前景。
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