Abstract：
Lateral semicircular canal (LSCC) malformations represent one of the most common types of inner ear malformation. As many cases of LSCC malformations are asymptomatic, detailed vestibular functions in such cases remain unclear. We present a case with bilateral LSCC malformations for whom the function of each vestibular organ was evaluated by caloric testing, video Head Impulse Test (vHIT) and vestibular evoked myogenic potentials (VEMP). Caloric testing showed canal paresis of the left side, whereas vHIT showed bilateral normal semicircular canal function. The results of VEMP indicated left saccular dysfunction. Discrepancies in caloric testing and vHIT results were observed and these discrepancies are thought to be due to endolymphatic hydrops rather than vestibular hypofunction, similar to that in Meniere disease.
摘要：
外侧半规管（LSCC）畸形是最常见的内耳畸形之一。由于许多LSCC畸形病例是无症状的，此类病例的详细前庭功能仍不清楚.我们介绍了一个双侧LSCC畸形的病例，通过热量测试评估了每个前庭器官的功能。视频头部脉冲测试（vHIT）和前庭诱发肌源性电位（VEMP）。热量测试显示左侧管麻痹，而vHIT显示双侧半规管功能正常。VEMP结果提示左囊功能障碍。观察到热量测试和vHIT结果的差异，这些差异被认为是由于内淋巴积水而不是前庭功能减退。类似于梅尼埃病。
