Abstract：
Granulomatosis with polyangiitis (GPA) is characterized by necrotizing vasculitis of small and medium sized vessels and is rarely present in the pediatric population. Cardiac manifestations in pediatric patients with GPA are extremely uncommon, with only two known reported cases associated with coronary artery aneurysms (Rehani and Nelson in Pediatrics 147:e20200932, 2021, https://doi.org/10.1542/peds.2020-0932 ;Aghaei Moghadam et al. in Case Rep Cardiol 2020:3417910, 2020, https://doi.org/10.1155/2020/3417910 ). We report a case of a 14-year-old male who presented with a 1 month history of fatigue and shortness of breath. He ultimately was found to have multiple giant coronary aneurysms in both the left and right coronaries including a giant aneurysm in the posterior descending; this has not been previously reported. The case highlights the need for complete multi-modality imaging of the coronary arteries in patients with GPA.
摘要：
肉芽肿性多血管炎（GPA）的特征是中小型血管的坏死性血管炎，在儿科人群中很少出现。患有GPA的儿科患者的心脏表现极为罕见，仅有两例已知报告的与冠状动脉动脉瘤相关的病例(Rehani和NelsoninPediatrics147:e20200932,2021,https://doi.org/10.1542/peds.2020-0932;AghaeiMoghadam等。在案例代表Cardiol2020：3417910，2020，https://doi.org/10.1155/2020/3417910）。我们报告了一例14岁男性，有1个月的疲劳和呼吸急促病史。他最终被发现在左冠状动脉和右冠状动脉都有多个巨大的冠状动脉瘤，包括后下降部的巨大动脉瘤；以前没有报道过。该病例强调了GPA患者需要对冠状动脉进行完整的多模态成像。
