关键词: Aicardi syndrome Corpus callosum Peripapillary chorioretinal lacunae Peripheral retina nonperfusion Stalk tissue Tractional retinal detachment Aicardi syndrome Corpus callosum Peripapillary chorioretinal lacunae Peripheral retina nonperfusion Stalk tissue Tractional retinal detachment

来  源:   DOI:10.1016/j.ajoc.2022.101467   PDF(Pubmed)

Abstract:
UNASSIGNED: To report a rare case of Aicardi syndrome presenting with concurrent peripheral retina nonperfusion with 360-degree neovascularization in the right eye and stalk tissue with a peripapillary fibrovascular membrane and tractional retinal detachment (TRD) in the left eye.
UNASSIGNED: A one-month-old girl was referred for an ophthalmic evaluation to confirm the diagnosis of Aicardi syndrome due to abnormal brain magnetic resonance imaging. A 360-degree circumferential peripheral avascular retina with extensive neovascularization was present in the right eye. Stalk tissue with fibrovascular proliferation causing TRD was found in the left fundus. The retina of the right eye became quiescent after completing peripheral laser photocoagulation. The detached retina in the left eye was flattened, and the peripapillary chorioretinal lacunae became visible one year after surgical removal of the traction. In addition, the axial length growth of the left eye regained.
UNASSIGNED: This is a rare case of Aicardi syndrome with concurrent peripapillary fibrovascular traction in one eye and peripheral retina nonperfusion in the other eye. Surgical intervention is vital not only for removing the traction and flattening the retina but also for promoting continual growth of the eyeball.
摘要:
未经证实:报告一例罕见的Aicardi综合征,其右眼周边视网膜无灌注并伴有360度新生血管形成,左眼茎组织伴有乳头周围纤维血管膜和牵张性视网膜脱离(TRD)。
UNASSIGNED:一名一个月大的女孩因脑部磁共振成像异常而被转诊接受眼科评估,以确认诊断为Aicardi综合征。右眼存在360度周围无血管视网膜,伴有广泛的新生血管形成。在左侧眼底发现有纤维血管增生引起TRD的茎组织。右眼的视网膜在完成周边激光光凝后变得静止。左眼脱离的视网膜变平了,在手术切除牵引一年后,乳头周围脉络膜视网膜腔隙变得可见。此外,左眼的轴向长度增长恢复。
UNASSIGNED:这是一例罕见的Aicardi综合征,其中一只眼并发乳头状周围纤维血管牵引,另一只眼周边视网膜无灌注。手术干预不仅对于消除牵引和使视网膜变平至关重要,而且对于促进眼球的持续生长至关重要。
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