PDF(Pubmed)
Abstract：
UNASSIGNED: This study sought to analyze the computed tomography (CT) and magnetic resonance imaging (MRI) characteristics of the classical triad elements and the associated anomalies in pediatric complete Currarino syndrome (CS) to evaluate the advantages and disadvantages of the 2 different imaging methods in displaying the abnormalities of this disease.
UNASSIGNED: The clinical and radiological features of 32 pediatric patients with complete CS diagnosed histologically and/or radiologically were retrospectively analyzed.
UNASSIGNED: All 32 complete CS patients presented with the classical triad of congenital anorectal malformation (ARM), sacral agenesis, and presacral mass. Anal atresia, which is the most common congenital ARM, was observed in 19 of the 32 patients (59.4%). Sacral agenesis was mainly type IV (75%). Among the presacral masses, true tumors and pseudotumors accounted for about half each. All of the 15 true tumors were presacral teratomas. Twenty-five patients had associated anomalies, including tethered cord, filum lipoma, and hydronephrosis. Twenty-four patients underwent both CT and MRI examinations. While CT was better than MRI in displaying sacral anomaly (P<0.05), MRI was more sensitive than CT at detecting presacral mass, spinal dysraphism, and congenital anal atresia (P<0.05).
UNASSIGNED: CT and MRI have different efficiencies at displaying the abnormalities of the complete CS. As a non-invasive method, MRI has significant advantages in diagnosing complete CS, especially in revealing the details of ARM, presacral mass, and associated spinal dysraphism.
UNASSIGNED: The clinical and radiological features of 32 pediatric patients with complete CS diagnosed histologically and/or radiologically were retrospectively analyzed.
UNASSIGNED: All 32 complete CS patients presented with the classical triad of congenital anorectal malformation (ARM), sacral agenesis, and presacral mass. Anal atresia, which is the most common congenital ARM, was observed in 19 of the 32 patients (59.4%). Sacral agenesis was mainly type IV (75%). Among the presacral masses, true tumors and pseudotumors accounted for about half each. All of the 15 true tumors were presacral teratomas. Twenty-five patients had associated anomalies, including tethered cord, filum lipoma, and hydronephrosis. Twenty-four patients underwent both CT and MRI examinations. While CT was better than MRI in displaying sacral anomaly (P<0.05), MRI was more sensitive than CT at detecting presacral mass, spinal dysraphism, and congenital anal atresia (P<0.05).
UNASSIGNED: CT and MRI have different efficiencies at displaying the abnormalities of the complete CS. As a non-invasive method, MRI has significant advantages in diagnosing complete CS, especially in revealing the details of ARM, presacral mass, and associated spinal dysraphism.
摘要：
UNASSIGNED：本研究旨在分析经典三联征元素的计算机断层扫描（CT）和磁共振成像（MRI）特征以及小儿完全性Currarino综合征（CS）的相关异常，以评估两种不同成像方法在显示该疾病异常方面的优缺点。
UNASSIGNED：回顾性分析了32例经组织学和/或放射学诊断为完全CS的儿科患者的临床和放射学特征。
UNASSIGNED：所有32例完整的CS患者均表现为先天性肛门直肠畸形（ARM）的经典三联征，骶骨发育不全,和骶前肿块。肛门闭锁,这是最常见的先天性手臂，在32例患者中的19例（59.4%）中观察到。骶骨发育不全主要为IV型(75%)。在骶前肿块中，真性肿瘤和假性肿瘤各占一半。15例真性肿瘤均为骶前畸胎瘤。25名患者有相关异常，包括系绳,丝状脂肪瘤，和肾积水.24例患者接受了CT和MRI检查。而CT显示骶骨异常优于MRI(P<0.05),MRI在检测骶前肿块方面比CT更敏感，脊髓发育不良,先天性肛门闭锁(P<0.05)。
UNASSIGNED：CT和MRI在显示完整CS异常方面具有不同的效率。作为一种非侵入性方法，MRI在诊断全CS方面具有显著优势,特别是在揭示ARM的细节方面，骶前肿块,和相关的脊髓发育不良。
UNASSIGNED：回顾性分析了32例经组织学和/或放射学诊断为完全CS的儿科患者的临床和放射学特征。
UNASSIGNED：所有32例完整的CS患者均表现为先天性肛门直肠畸形（ARM）的经典三联征，骶骨发育不全,和骶前肿块。肛门闭锁,这是最常见的先天性手臂，在32例患者中的19例（59.4%）中观察到。骶骨发育不全主要为IV型(75%)。在骶前肿块中，真性肿瘤和假性肿瘤各占一半。15例真性肿瘤均为骶前畸胎瘤。25名患者有相关异常，包括系绳,丝状脂肪瘤，和肾积水.24例患者接受了CT和MRI检查。而CT显示骶骨异常优于MRI(P<0.05),MRI在检测骶前肿块方面比CT更敏感，脊髓发育不良,先天性肛门闭锁(P<0.05)。
UNASSIGNED：CT和MRI在显示完整CS异常方面具有不同的效率。作为一种非侵入性方法，MRI在诊断全CS方面具有显著优势,特别是在揭示ARM的细节方面，骶前肿块,和相关的脊髓发育不良。
