PDF(Pubmed)
Abstract：
Congenital nasal pyriform aperture stenosis (CNPAS) is a rare cause of respiratory distress in newborns. This paper reports a case of severe CNPAS that required endotracheal intubation immediately after birth, and eventually, surgical intervention. At birth, the width of the pyriform aperture was only 4 mm, and the patient was completely unable to breathe through his nose. We performed tracheostomy at 23 days of age and waited for the patient to grow, but at 56 days of age, the width of the pyriform aperture was not sufficient (6 mm) for the patient to breathe through his nose. Therefore, surgical dilation of the pyriform aperture by a sublabial approach was performed on day 79 after birth, and the width was increased to 14 mm. Postoperative stent placement was performed for two weeks. After the removal of the stents, the patient could finally breathe through his nose, and the postoperative course was uneventful, with no restenosis after four months. CNPAS is a rare cause of nasal obstruction, but it can cause respiratory distress in infants because they are dependent on nasal breathing. Conservative treatments are initially recommended for CNPAS; however, in severe cases where conservative treatments are ineffective, surgical treatment is recommended.
摘要：
先天性鼻梨形孔狭窄（CNPAS）是新生儿呼吸窘迫的罕见原因。本文报道一例出生后立即需要气管插管的严重CNPAS，最终，手术干预。出生时,梨形孔的宽度只有4毫米，病人完全无法通过鼻子呼吸。我们在23天大的时候做了气管切开术，等待病人成长，但是在56岁的时候，梨形孔的宽度(6毫米)不足以让病人通过鼻子呼吸。因此,出生后第79天通过阴唇入路手术扩张梨形孔，宽度增加到14毫米。术后放置支架2周。移除支架后,病人终于可以用鼻子呼吸了,术后过程平稳，四个月后没有再狭窄.CNPAS是一种罕见的鼻塞病因,但它可以导致呼吸窘迫的婴儿，因为他们是依赖鼻呼吸。最初建议对CNPAS进行保守治疗；然而，在保守治疗无效的严重病例中，建议手术治疗。
