Abstract：
Obstructed hemivagina and ipsilateral renal agenesis (OHVIRA) is a rare congenital malformation of the female reproductive organs, including uterine dysplasia, blind hemivagina, and ipsilateral renal dysplasia. It has a serious impact on patients\' quality of life and fertility. We report a rare case of OHVIRA with a complete septate uterus, ectopic dysplasia of the left kidney, left ectopic ureter, and three oblique vaginal septa. The dysplastic left kidney and the ectopic ureter were removed during laparoscopy. In addition, the two layers of vaginal septa, which were ignored in the past 10 years, were removed by hysteroscopy. As the detection rate of OHVIRA has gradually increased, manifestations that previous classification systems could not recapitulate have emerged. By retrieving the relevant cases, we have tried to propose a new classification system, which would allow clinicians to have a complete understanding of the manifestations of OHVIRA and would be helpful in the treatment of patients.
摘要：
阻塞的半阴道和同侧肾发育不全（OHVIRA）是女性生殖器官罕见的先天性畸形，包括子宫发育不良,失明的半阴道,同侧肾发育不良.严重影响患者的生活质量和生育能力。我们报告了一例罕见的OHVIRA病例，有一个完整的纵隔子宫，左肾异位发育不良,左输尿管异位,和三个斜阴道隔膜。在腹腔镜检查期间切除了发育不良的左肾和异位输尿管。此外,两层阴道隔膜，在过去的10年里被忽视了，被宫腔镜切除。随着OHVIRA的检出率逐渐提高,以前的分类系统无法概括的表现形式已经出现。通过检索相关案例，我们试图提出一个新的分类系统，这将使临床医生完全了解OHVIRA的表现，并有助于患者的治疗。
