关键词: Aortopathy Bicuspid aortic valve Classification Nomenclature

Mesh : Aorta / diagnostic imaging surgery Aortic Diseases / classification diagnostic imaging surgery Aortic Valve / abnormalities diagnostic imaging surgery Aortography Bicuspid Aortic Valve Disease / classification diagnostic imaging surgery Cardiac Imaging Techniques Consensus Humans Phenotype Predictive Value of Tests Prognosis Terminology as Topic

来  源:   DOI:10.1016/j.jtcvs.2021.05.008   PDF(Sci-hub)

Abstract:
This International evidence-based nomenclature and classification consensus on the congenital bicuspid aortic valve and its aortopathy recognizes 3 types of bicuspid aortic valve: 1. Fused type, with 3 phenotypes: right-left cusp fusion, right-non cusp fusion and left-non cusp fusion; 2. 2-sinus type with 2 phenotypes: Latero-lateral and antero-posterior; and 3. Partial-fusion or forme fruste. This consensus recognizes 3 bicuspid-aortopathy types: 1. Ascending phenotype; root phenotype; and 3. extended phenotypes.
摘要:
这项关于先天性二叶主动脉瓣及其主动脉瓣病的国际循证命名和分类共识识别了3种类型的二叶主动脉瓣:1.熔融型,有3种表型:左右尖点融合,右非尖点融合和左非尖点融合;2.具有2种表型的2窦型:横向外侧和前后侧;和3.部分融合的或形成圆果。该共识承认3种二尖瓣-主动脉病类型:1.上升表型;根表型;和3.扩展表型。
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