Abstract:
Biliary hamartomas (BHs) are rare malformative cystic/cystic-like lesions of the liver affecting the biliary tree, named after Hanns von Meyenburg who described them for the first time and still known with this eponym to this day. They usually lack clinical symptoms, and abnormalities in liver function tests are unusual; thus, it is typically an incidental finding of liver imaging. Despite being benign lesions, BHs can pose clinical challenges; the first one is differential diagnosis with other more relevant pathological conditions. Therefore, knowledge of MR imaging findings of BHs is helpful for a prompt and correct diagnosis, avoiding unnecessary invasive procedures and/or an excessive number of radiological investigations. This pictorial review is aimed to depict the most typical MR imaging features of multiple biliary hamartomas (von Meyenburg Complex), in order to familiarize the diagnosis and facilitate the differentiation from other hepato-biliary cystic diseases.
摘要:
胆道错构瘤(BHs)是罕见的肝脏畸形囊性/囊样病变,影响胆道树,以汉斯·冯·梅恩堡(HannsvonMeyenburg)的名字命名,他第一次描述了它们,至今仍以这个名字而闻名。他们通常缺乏临床症状,肝功能检查异常是不寻常的;因此,它通常是肝脏成像的偶然发现。尽管是良性病变,BHs可能会带来临床挑战;第一个是与其他更相关的病理状况的鉴别诊断。因此,了解BHs的MR影像学表现有助于及时正确的诊断,避免不必要的侵入性程序和/或过多的放射学检查。这篇图片综述旨在描述多发性胆道错构瘤(vonMeyenburgComplex)的最典型的MR成像特征,为了熟悉诊断并促进与其他肝胆囊性疾病的鉴别。