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Abstract：
BACKGROUND: Congenital upper limb Amelia is one of the extremely rare conditions in the world. Defined as complete absence of a limb which may present as isolated defect or as a part of syndrome with associated anomalies.
METHODS: We report a case of a medically free 6-year-old boy with bilateral upper limb Amelia associated with right thoracolumbar idiopathic Scoliosis.
CONCLUSIONS: Treatment for early onset scoliosis includes either posterior spinal fusion and instrumentation, or Vertical Expandable Prosthetic Titanium Rib (VEPTR). The choice of care for our patient was decided to be VEPTR alone as definitive management. Up to our knowledge, there are very scanty articles published regarding treatment for such cases.
CONCLUSIONS: Patient underwent vertical expandable prosthetic titanium rib (VEPTR) application for his large 45-degree curve as a definitive treatment and still have his preoperative physical functions, in terms of using lower limbs in daily living activities.
METHODS: We report a case of a medically free 6-year-old boy with bilateral upper limb Amelia associated with right thoracolumbar idiopathic Scoliosis.
CONCLUSIONS: Treatment for early onset scoliosis includes either posterior spinal fusion and instrumentation, or Vertical Expandable Prosthetic Titanium Rib (VEPTR). The choice of care for our patient was decided to be VEPTR alone as definitive management. Up to our knowledge, there are very scanty articles published regarding treatment for such cases.
CONCLUSIONS: Patient underwent vertical expandable prosthetic titanium rib (VEPTR) application for his large 45-degree curve as a definitive treatment and still have his preoperative physical functions, in terms of using lower limbs in daily living activities.
摘要：
背景：先天性上肢Amelia是世界上极为罕见的疾病之一。定义为肢体完全缺失，可能表现为孤立的缺陷或作为伴随异常的综合征的一部分。
■我们报告一例6岁男孩，双侧上肢Amelia伴右侧胸腰椎特发性脊柱侧凸。
结论：早发性脊柱侧凸的治疗包括后路脊柱融合术和器械，或垂直可扩展的人造钛肋（VEPTR）。我们的患者的护理选择被决定为单独的VEPTR作为确定的管理。根据我们的知识，关于这种情况的治疗，发表的文章很少。
结论：患者接受了垂直可扩张假体钛肋骨（VEPTR）的应用，因为他的大45度曲线作为明确的治疗方法，并且仍然具有术前身体功能，在日常生活活动中使用下肢。
■我们报告一例6岁男孩，双侧上肢Amelia伴右侧胸腰椎特发性脊柱侧凸。
结论：早发性脊柱侧凸的治疗包括后路脊柱融合术和器械，或垂直可扩展的人造钛肋（VEPTR）。我们的患者的护理选择被决定为单独的VEPTR作为确定的管理。根据我们的知识，关于这种情况的治疗，发表的文章很少。
结论：患者接受了垂直可扩张假体钛肋骨（VEPTR）的应用，因为他的大45度曲线作为明确的治疗方法，并且仍然具有术前身体功能，在日常生活活动中使用下肢。
