Asymmetrically severe internal auditory canal hypoplasia: A case report.

• 发表时间: May 2020
• 来源期刊: Radiol Case Rep
• DOI: 10.1016/j.radcr.2020.01.037
• PMID: 32123553
• 文章类型: Case Reports
• 作者列表: Martin JW,Wishka C,Thompson M,Djalilian HR,Floriolli D,Senturk C,Hasso A

关键词: Incomplete partition; Internal auditory canal hypoplasia; Neuroradiology; SNHL; Sensorineural hearing loss

Abstract

We present a case of an otherwise healthy 20-month-old with congenital sensorineural hearing loss. CT and MR imaging demonstrated bilateral asymmetrically severe hypoplasia of the internal auditory canals and vestibulocochlear nerves. Additional developmental inner ear anomalies were present in this patient, including unilateral semicircular canal hypoplasia and suspected bilateral cochlear hypoplasia. The patient retained normal facial nerve function bilaterally. We highlight the current research and understanding of congenital IAC abnormalities.