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Abstract：
UNASSIGNED: Hirschsprung\'s disease (HD) is uncommon in adulthood. In this study, we describe the management of two cases of adult Hirschsprung\'s disease treated with transanal colonic pull-through procedure followed by a delayed coloanal anastomosis.
UNASSIGNED: This was a retrospective (December 2016 to Jun 2019) study included two cases of adult HD with confirmed Hirschsprung disease who underwent surgery at Zinder National hospital, Niger. The registration number is researchregistry 5174.
UNASSIGNED: These were two patients aged 21 years (male) and 22 years (female) admitted to the emergency department with an acute bowel obstruction. The history finds a delayed passage of meconium at birth with a history of long-standing recurrent constipation since early childhood for the 2 patients. A lateral colostomy was performed urgently in both patients and the barium enema revealed a disparity of the sigmoid colon with corn shaped transition zone. Histologic examination of the biopsy specimen confirmed the diagnosis of HD. Surgery was done according to transanal endorectal pull-through procedure followed by delayed coloanal anastomosis. Patients were regularly followed over a period of 16 months. Constipation was gone, no continence problem was reported and quality of life was rated satisfactory.
UNASSIGNED: The discovery of Hirschsprung\'s disease is rare in adulthood. Transanal endorectal pull-through procedure followed by delayed coloanal anastomosis with conventional surgery is a suitable option for the treatment of HD and gives a good result.
UNASSIGNED: This was a retrospective (December 2016 to Jun 2019) study included two cases of adult HD with confirmed Hirschsprung disease who underwent surgery at Zinder National hospital, Niger. The registration number is researchregistry 5174.
UNASSIGNED: These were two patients aged 21 years (male) and 22 years (female) admitted to the emergency department with an acute bowel obstruction. The history finds a delayed passage of meconium at birth with a history of long-standing recurrent constipation since early childhood for the 2 patients. A lateral colostomy was performed urgently in both patients and the barium enema revealed a disparity of the sigmoid colon with corn shaped transition zone. Histologic examination of the biopsy specimen confirmed the diagnosis of HD. Surgery was done according to transanal endorectal pull-through procedure followed by delayed coloanal anastomosis. Patients were regularly followed over a period of 16 months. Constipation was gone, no continence problem was reported and quality of life was rated satisfactory.
UNASSIGNED: The discovery of Hirschsprung\'s disease is rare in adulthood. Transanal endorectal pull-through procedure followed by delayed coloanal anastomosis with conventional surgery is a suitable option for the treatment of HD and gives a good result.
摘要：
■先天性巨结肠病（HD）在成年期并不常见。在这项研究中,我们描述了2例成人先天性巨结肠经肛门结肠牵拉术后延迟结肠吻合术的治疗方法。
■这是一项回顾性研究（2016年12月至2019年6月），包括在Zinder国立医院接受手术的两例成人HD确诊为先天性巨结肠症。尼日尔。登记号是研究登记处5174。
■这两名患者分别为21岁（男性）和22岁（女性），因急性肠梗阻进入急诊科。病史发现2例患者出生时胎粪延迟通过，并有长期反复便秘的病史。两名患者均紧急进行了侧结肠造口术，钡灌肠显示乙状结肠与玉米形过渡区的差异。活检标本的组织学检查证实了HD的诊断。根据经肛门直肠内牵拉术进行手术，然后进行延迟结肠吻合术。患者定期随访16个月。便秘消失了,未报告出现尿失禁问题,生活质量评分令人满意.
■赫氏弹簧病的发现在成年期是罕见的。经肛门直肠内牵拉术，然后进行常规手术的延迟结肠吻合术是治疗HD的合适选择，效果良好。
■这是一项回顾性研究（2016年12月至2019年6月），包括在Zinder国立医院接受手术的两例成人HD确诊为先天性巨结肠症。尼日尔。登记号是研究登记处5174。
■这两名患者分别为21岁（男性）和22岁（女性），因急性肠梗阻进入急诊科。病史发现2例患者出生时胎粪延迟通过，并有长期反复便秘的病史。两名患者均紧急进行了侧结肠造口术，钡灌肠显示乙状结肠与玉米形过渡区的差异。活检标本的组织学检查证实了HD的诊断。根据经肛门直肠内牵拉术进行手术，然后进行延迟结肠吻合术。患者定期随访16个月。便秘消失了,未报告出现尿失禁问题,生活质量评分令人满意.
■赫氏弹簧病的发现在成年期是罕见的。经肛门直肠内牵拉术，然后进行常规手术的延迟结肠吻合术是治疗HD的合适选择，效果良好。
