A Case of Idiopathic Non-Cirrhotic Portal Hypertension in a Patient With a Left Ventricular Assist Device.

• 发表时间: Jan-Dec 2019
• 来源期刊: J Investig Med High Impact Case Rep
• DOI: 10.1177/2324709619878337
• PMID: 31554434
• 文章类型: Case Reports
• 作者列表: Kothari S,Kalinowski M,Shah N,Raddawi H

关键词: endoscopy; hepatic venous pressure gradient; left ventricular assist device; non-cirrhotic portal hypertension

Mesh: Esophageal and Gastric Varices / etiology; Heart-Assist Devices / adverse effects; Humans; Hypertension, Portal / diagnostic imaging etiology physiopathology; Liver / pathology; Male; Middle Aged; Pleural Effusion / diagnostic imaging etiology physiopathology; Portal Pressure; Tomography, X-Ray Computed; Ventricular Function, Right

Abstract

Idiopathic non-cirrhotic portal hypertension is a rare diagnosis caused by an unknown etiology with elevated intrahepatic portal pressures in the absence of underlying liver disease. We present a unique case of a 57-year-old male with a left ventricular assist device and preserved right ventricular function that was found to have an elevated hepatic venous pressure gradient and sequelae of portal hypertension without underlying liver disease. There is limited treatment available as management is primarily aimed toward preventing complications of the disease. This case highlights the need for further investigative research of this disease entity and its pathogenesis.