Prenatally Diagnosed Ventricular Inversion, Restrictive Ventricular Septal Defect, Pulmonary Stenosis, Hypertensive Left Ventricle and Double Outlet Right Ventricle: Case Report and Literature Review.

经肾前诊断的心室反转 ，限制性室间隔缺损,肺动脉狭窄,高血压左心室和右心室双出口 ： 病例报告并文献复习。

• 影响指数: 1.838
• 发表时间: Jan 2019
• 来源期刊: Pediatr Cardiol
• DOI: 10.1007/s00246-018-2048-8
• PMID: 30569250
• 文章类型: Case Reports
• 中科院分区: Q4
• 方向: 医学
• 作者列表: El-Asmar JM,Degheili JA,Al-Halabi E,Sklansky M

关键词: Complex fetal heart disease; Double-outlet right ventricle; Fetal echocardiography; Ventricular inversion

Mesh: Adult; Double Outlet Right Ventricle / diagnostic imaging; Echocardiography; Female; Fetal Heart / diagnostic imaging; Gestational Age; Heart Septal Defects, Ventricular / diagnostic imaging; Humans; Pregnancy; Pulmonary Valve Stenosis / diagnostic imaging; Ultrasonography, Prenatal / methods

Abstract

We herein describe, for the first time, the fetal presentation of a case of ventricular inversion, restrictive ventricular septal defect, pulmonary stenosis, hypertensive left ventricle and double outlet right ventricle at 34 weeks of gestational age. Postnatal echocardiography confirmed the prenatal diagnosis. The patient was subsequently successfully palliated with a left ventricle to pulmonary artery conduit. This report illustrates the importance of detailed fetal echocardiography to ensure appropriate delivery and neonatal management, and to optimize outcome.

摘要

我们在这里描述，第一次,胎儿出现的心室倒置病例,限制性室间隔缺损,肺动脉狭窄,胎龄34周时高血压左心室和右心室双出口。产后超声心动图证实产前诊断。随后，患者通过左心室至肺动脉导管成功缓解。本报告说明了详细的胎儿超声心动图检查的重要性，以确保适当的分娩和新生儿管理，优化结果。