关键词: Anasarca Castleman disease Fever Organomegaly Reticulin fibrosis TAFRO

Mesh : Castleman Disease / pathology Edema / pathology Fever / pathology Humans Pathologists Syndrome Thrombocytopenia / pathology

来  源:   DOI:10.1016/j.critrevonc.2018.05.015

Abstract:
TAFRO is an acrostic and includes thrombocytopenia (T), anasarca (A), fever (F), reticulin fibrosis (R) and organomegaly (O) (Takai et al., 2013). TAFRO syndrome has been described firstly by Takai in Japanese patients. However TAFRO cases have been reported from US, Europe and other countries (Takai et al., 2010; Iwaki et al., 2016; Abdo et al., 2014). Three major and at least one minor criteria and exclusion of infectious, rheumatologic and neoplastic diseases are required for the diagnosis of TAFRO. In fact TAFRO must be thought in clinically undiagnosed and unsolved problemmatic cases.
摘要:
TAFRO是一种肢端囊性疾病,包括血小板减少症(T),anasarca(A),发烧(F),网织蛋白纤维化(R)和器官肿大(O)(Takai等人。,2013).Takai首先在日本患者中描述了TAFRO综合征。然而,美国已经报道了TAFRO病例,欧洲和其他国家(Takai等人。,2010;Iwaki等人。,2016;Abdo等人。,2014).三个主要和至少一个次要标准和排除传染性,TAFRO的诊断需要风湿病和肿瘤疾病。实际上,在临床未诊断和未解决的问题病例中,必须考虑TAFRO。
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