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Abstract：
Primary pleomorphic xanthoastrocytoma (PXA) of the spinal cord is a rare slow growing tumor. To our knowledge, only five such cases have been reported in the literature till date. We report the clinical, radiological, and histopathological features of a spinal PXA in a 23-year-old female previously operated 5 years back for a spinal tumor, presented with weakness in lower limbs, sphincter incontinence and low back pain. Magnetic resonance imaging scan with contrast reveals an intramedullary lesion in the spinal cord from D8-D10 level. The patient was operated with reexploration of the previous incision, and gross total excision was achieved. Histopathology confirmed the diagnosis of PXA. Clinical and radiological follow-up is required to detect early recurrence. Adjunct radiotherapy or and chemotherapy should be considered only when there is postoperative residual or recurrence, however there are no definite guidelines in view of the rarity of this condition.
摘要：
脊髓原发性多形性黄色星形细胞瘤（PXA）是一种罕见的缓慢生长的肿瘤。据我们所知,迄今为止，文献中只报道了5例此类病例。我们报告临床，放射学,以及一名23岁女性的脊柱PXA的组织病理学特征，表现为下肢无力，括约肌失禁和腰痛。增强磁共振成像扫描显示D8-D10水平的脊髓髓内病变。患者进行了手术，重新探查了先前的切口，并实现了总切除。组织病理学证实了PXA的诊断。需要临床和放射学随访以检测早期复发。仅当术后残留或复发时，才应考虑辅助放疗或化疗。然而，鉴于这种情况的罕见性，没有明确的指导方针。
