关键词: bilobed involvement giant bullous emphysema pediatric placental transmogrification

Mesh : Adolescent Humans Lung / pathology Male Pulmonary Emphysema / pathology

来  源:   DOI:10.1177/1066896917714889

Abstract:
Giant bullous emphysema with placental transmogrification is an extremely rare entity, with 30 previously reported cases. Of these reported cases, it is typically identified with varied clinical and radiological impressions, presents in young adulthood to elderly, is always unilateral, and usually involves just one lobe. Despite the unknown pathogenesis, this diagnosis carries an excellent prognosis and is curative with complete resection. The pulmonary placental transmogrification is histologically indistinguishable from placental origin. Although not necessary to utilize because of the male predominance and no reported association, immunohistochemical stains can be used to prove lung origin. We report an extremely rare case of 2-lobe involvement of giant bullous emphysema with placental transmogrification in a boy 14 years of age, who is the youngest diagnosed patient with this lung abnormality.
摘要:
巨大的大疱性肺气肿伴胎盘移位是一种极其罕见的实体,有30例以前报告的病例。在这些报告的病例中,它通常具有不同的临床和放射学印象,在年轻时送给老年人,总是单方面的,通常只涉及一个肺叶。尽管发病机制未知,该诊断预后良好,完全切除可治愈。肺胎盘移位在组织学上与胎盘起源没有区别。虽然没有必要利用,因为男性占主导地位,没有报告的关联,免疫组织化学染色可用于证明肺起源。我们报告了一个极为罕见的病例,在一个14岁的男孩中,巨大的大疱性肺气肿伴胎盘移位,是最年轻的肺部异常患者.
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