Congenital nasal pyriform aperture stenosis in association with solitary median maxillary central incisor: unique radiologic features.

• 发表时间: Sep 2016
• 来源期刊: Radiol Case Rep
• DOI: 10.1016/j.radcr.2016.06.004
• PMID: 27594945
• 文章类型: Case Reports
• 作者列表: Yang S,Orta P,Renk EM,Inman JC

关键词: Congenital nasal obstruction; Congenital nasal pyriform aperture stenosis; Hypothalamo-pituitary axis; Solitary median maxillary central incisor

Abstract

Solitary median maxillary central incisor (SMMCI) coexists in 34%-65% of patients initially diagnosed with congenital nasal pyriform aperture stenosis. SMMCI, a genetic syndrome, warrants consideration for further screening because of its high prevalence of other diagnostic possibilities-specifically central defects, like nasal obstruction and hypothalamo-pituitary axis abnormalities. We report on a presentation of SMMCI with congenital nasal pyriform aperture stenosis which highlights the unique radiologic features and notes the relationship between these two central associated findings in the literature.