Recurrent pneumothorax in a young female with pulmonary lymphangiomyomatosis: a case report and overview of literature.

1 例年轻女性肺淋巴管肌瘤病复发性气胸 1 例并文献综述.

• 发表时间: Jan 2014
• 来源期刊: J Family Med Prim Care
• DOI: 10.4103/2249-4863.130336
• PMID: 24791247
• 文章类型: Case Reports
• 作者列表: Jain VV,Gupta OP,Jajoo S,Khiangate B

关键词: Cystic disease; lymphangiomyomatosis; pneumothorax; pulmonary

Abstract

Lymphangiomyomatosis (LAM) is a rare cystic interstitial lung disease that exclusively affects women of child bearing age and is associated with vascular proliferation of smooth muscle cells in the lung. We report a case of young female with pulmonary LAM presenting with recurrent pneumothorax.

摘要

淋巴管肌瘤病（LAM）是一种罕见的囊性间质性肺病，仅影响育龄妇女，并与肺中平滑肌细胞的血管增殖有关。我们报告了一例年轻女性的肺部LAM，表现为复发性气胸。