关键词: Complications Cystic Fibrosis Diabetic myonecrosis Physiopathology

Mesh : Adult Cystic Fibrosis / complications diagnostic imaging Diabetes Complications / complications diagnostic imaging Humans Male Muscular Diseases / diagnostic imaging etiology Necrosis Radiography

来  源:   DOI:10.3121/cmr.2013.1124   PDF(Pubmed)

Abstract:
Cystic fibrosis is a recessive autosomal disease caused by mutations in the cystic fibrosis transmembrane conductance regulator gene. Cystic fibrosis-related diabetes (CFRD) is a common comorbidity of cystic fibrosis. Diabetic myonecrosis is a rare self-limited complication of poorly controlled diabetes mellitus that commonly presents with acute, intense pain and swelling of lower extremities and responds well to conservative management. We report the first case of diabetic myonecrosis in a patient with CFRD.
摘要:
囊性纤维化是由囊性纤维化跨膜传导调节基因的突变引起的隐性常染色体疾病。囊性纤维化相关糖尿病(CFRD)是囊性纤维化的常见合并症。糖尿病性心肌坏死是一种罕见的自我限制的糖尿病控制不佳的并发症,通常表现为急性,下肢剧烈疼痛和肿胀,对保守治疗反应良好。我们报告了第一例CFRD患者的糖尿病性心肌坏死。
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