PDF(Pubmed)
Abstract：
Von Meyenburg Complexes (VMCs) is a rare clinicopathologic entity, consisting of small (<1.5cm), usually multiple and nodular cystic lesions. VMCs typically cause no symptoms or disturbances in liver function and thus in most instances they are diagnosed incidentally. We present four VMCs cases, each with a distinct clinical presentation. In two of our cases, VMCs caused mild, non-specific abdominal symptoms, including diffuse abdominal pain and discomfort. In the other two cases, in a 60-year-old woman and a 25-year-old man, the clinical presentation was implicative of an infectious hepatic process reminiscent of cholangitis and liver abscesses respectively. In each case the diagnosis was based on magnetic resonance imaging and magnetic resonance cholangiopancreatography findings showing multiple hyper-intense cystic nodules not communicating with the biliary tree. Physicians should be aware of the entire clinical spectrum of VMCs and its unique radiologic features in order to differentiate VMCs from other cystic liver lesions.
摘要：
冯·梅恩堡复合物（VMC）是一种罕见的临床病理实体，由小（<1.5cm）组成，通常是多发性和结节性囊性病变。VMC通常不会引起肝功能的症状或紊乱，因此在大多数情况下，它们是偶然诊断的。我们提出了四个VMC案例，每个都有不同的临床表现。在我们的两个案例中，VMC引起轻度，非特异性腹部症状，包括弥漫性腹痛和不适。在其他两种情况下，一个60岁的女人和一个25岁的男人，临床表现涉及感染性肝过程，分别让人联想到胆管炎和肝脓肿。在每种情况下，诊断均基于磁共振成像和磁共振胰胆管造影发现，显示多个高强度囊性结节与胆道树不连通。医生应该了解VMC的整个临床范围及其独特的放射学特征，以便将VMC与其他囊性肝脏病变区分开来。
